Endobronchial malignant fibrous histiocytoma: case report of an unusual presentation and palliative flexible bronchoscopic resection.

نویسندگان

  • Jung-Hyun Kim
  • Sang-Ho Cho
  • Eun-Kyung Kim
  • Ji-Hyun Lee
  • Hye-Cheol Jeong
چکیده

Primary malignant fibrous histiocytoma (MFH) of the lung is a very rare neoplasm that usually presents as a parenchymal mass. Here we report an unusual case of primary MFH of the bronchus, showing relatively benign clinical features. We performed a palliative resection via flexible bronchoscopy, using a polypectomy snare. The patient has survived for over 2 years after being diagnosed with an endobronchial mass, later found to be MFH, and 14 months post-debulking. There is a possibility that endobronchial MFH has a more favorable prognosis than MFH of other origins. If this is true, interventional bronchoscopy can be a reasonable option for non-operable cases of MFH.

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عنوان ژورنال:
  • Respiratory care

دوره 58 8  شماره 

صفحات  -

تاریخ انتشار 2013